fever plus CLS syndrome: cytopenia-lymphadenopathy-splenomegaly


lymphoma + include „classic“ lymphomas, MCD (HHV-8 asoc, + HIV), lymphoproliferative diseases. Some myeloproliferative diseases as some MDS forms may also have CLS presentations w or w/o HLH.
RES reticulo-endothelial system RHS reticulo-histiocytic system



































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